Abstract

Case Report

Sinonasal Myxoma Extending into the Orbit in a 4-Year Old: A Case Presentation

Julian A Purrinos* and Ramzi Younis

Published: 30 July, 2024 | Volume 8 - Issue 2 | Pages: 075-077

Background: Sinonasal myxomas are exceptionally rare benign tumors in pediatric patients. This report presents the case of a 4-year-old boy diagnosed with a sinonasal myxoma extending into the right orbit.
Case presentation: The patient’s clinical presentation included moderate-angle esotropia and ocular torticollis. Advanced imaging revealed an expansile lesion in the right posterior ethmoid cavity with orbital involvement. The differential diagnosis considered included malignancies such as rhabdomyosarcoma and lymphoma, as well as benign neoplasms and inflammatory changes. A biopsy confirmed the diagnosis of sinonasal myxoma. The patient underwent a wide local resection performed by a multidisciplinary team, leading to a confirmed histopathological diagnosis of sinonasal myxoma.
Conclusion: This case highlights the diagnostic challenges and the importance of thorough clinical and radiologic evaluation in pediatric patients with unusual ocular symptoms. The report underscores the need for a multidisciplinary approach in managing rare neoplasms such as sinonasal myxomas.

Read Full Article HTML DOI: 10.29328/journal.acr.1001099 Cite this Article Read Full Article PDF

Keywords:

Pediatric sinonasal myxoma; Pediatric orbital tumor; Differential diagnosis in pediatrics; Head and neck benign tumor in children; Pediatric rhinology

References

  1. Bhama PK, Manning SC, Cole B, Moe KS. Sinonasal myxoma involving the anterior skull base in an infant: A case report. Int J Pediatr Otorhinolaryngol Extra. 2012;7(1):26-29. Available from: https://doi.org/10.1016/j.pedex.2011.09.002
  2. Canalis RF, Smith GA, Konrad HR. Myxomas of the head and neck. Arch Otolaryngol. 1976;102(5):300-305. Available from: https://doi.org/10.1001/archotol.1976.00780100086012
  3. Safadi A, Fliss DM, Issakov J, Kaplan I. Infantile sinonasal myxoma: a unique variant of maxillofacial myxoma. J Oral Maxillofac Surg. 2011;69(2):553-558. Available from: https://doi.org/10.1016/j.joms.2010.10.007
  4. Prasannan L, Warren L, Herzog CE, Lopez-Camarillo L, Frankel L, Goepfert H. Sinonasal Myxoma. J Pediatr Hematol Oncol. 2005;27(2):90-92. Available from: https://doi.org/10.1097/01.mph.0000153443.36193.de
  5. Heffner DK. Problems in pediatric otorhinolaryngic pathology. I. Sinonasal and nasopharyngeal tumors and masses with myxoid features. Int J Pediatr Otorhinolaryngol. 1983;5:77-91. Available from: https://doi.org/10.1016/s0165-5876(83)80010-x
  6. Odintsov I, Dong F, Guenette J, et al. Infantile Sinonasal Myxoma Is Clinically and Genetically Distinct From Other Myxomas of the Craniofacial Bones and From Desmoid Fibromatosis. Am J Surg Pathol. 2023;47(11):1301-1315. Available from: https://doi.org/10.1097/pas.0000000000002119
  7. Lo Muzio L, Nocini P, Favia G, Procaccini M, Mignogna MD. Odontogenic myxoma of the jaws: a clinical, radiologic, immunohistochemical, and ultrastructural study. Oral Surg Oral Med Oral Pathol Oral Radiol Endod. 1996;82(4):426-33. Available from: https://doi.org/10.1016/s1079-2104(96)80309-x
  8. Mewar P, González-Torres KE, Jacks TM, Foss RD. Sinonasal Myxoma: A Distinct Lesion of Infants. Head Neck Pathol. 2020;14(1):212-219. Available from: https://doi.org/10.1007/s12105-018-0989-0
  9. Velez Torres JM, Mata DA, Briski LM, Green DC, Cloutier JM, Kerr DA, et al. Sinonasal Myxoma: A Distinct Entity or a Myxoid Variant of Desmoid Fibromatosis? Mod Pathol. 2023;36(7):100189. Available from: https://doi.org/10.1016/j.modpat.2023.100189

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